Pulmonary hypertension associated with Sjögren's syndrome. Case report

Authors

DOI:

https://doi.org/10.18537/RFCM.43.01.06

Keywords:

pulmonary hypertension, immune system, connective tissue diseases

Abstract

Introduction: Patients with connective tissue diseases (CTD) may present various forms of pulmonary hypertension (PH), and it is currently recognized that inflammatory processes play a crucial role in their development and progression.

Clinical case: This is a case of a 19-year-old woman with progressive dyspnea since 2019. On physical examination, heart murmurs are heard: in the aortic (II/VI) and tricuspid (I/VI) foci. Laboratory studies report positive ANA 1/320 with fine granular pattern, Anti-Ro >300 and SSA >200. Cardiac catheterization revealed severe pulmonary arterial hypertension, venocapillary hypertension.

Conclusions: CTD affects each patient individually, especially in their cardiovascular and respiratory systems, although it can present symptoms of dryness and arthralgia in a Sjögren's syndrome associated with PH.

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Published

2025-04-01

Issue

Vol. 43 No. 1 (2025): Revista de la Facultad de Ciencias Médicas de la Universidad de Cuenca

Section

Clinical Case

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Copyright (c) 2025 Ana Lucia Guamán Mizhirumbay , Inga Lojano Johana Priscila, Leydy Aracely Rodas Orellana

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